Polyglandular autoimmune syndrome-type I.

نویسندگان

Rajesh R Joshi

Sudha Rao

S S Prabhu

چکیده

Polyglandular autoimmune syndrome type I is a rare disorder characterized by mucocutaneous candidiasis (MC), hypoparathyroidism (HP) and adrenal insufficiency , requiring regular follow up as the components of the syndrome appear at different age groups. We report a six and half year boy having this syndrome and presenting with MC, HP and ectodermal dystrophy.

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